Gene Information

PALB2

partner and localizer of BRCA2 [Source:HGNC Symbol;Acc:HGNC:26144]

protein_codingChromosome 16ENSG00000083093

Overview

PALB2 variants are associated with 5 diseases including familial pancreatic carcinoma and Fanconi anemia and 3 others, with 27 documented clinical phenotypes.


Associated Diseases

The PALB2 gene is associated with 5 medical conditions, including:

familial pancreatic carcinoma

MONDO:0015278

Fanconi anemia

MONDO:0019391

hereditary breast carcinoma

MONDO:0016419

chordoma

MONDO:0008978

hereditary breast ovarian cancer syndrome

MONDO:0003582


Clinical Phenotypes

Research has identified 27 phenotypic features associated with PALB2 variants:

View all


ClinVar Variants

ClinVar contains 10 variants associated with PALB2. Below are some notable variants:

NM_024675.4(PALB2):c.2609del (p.Val870fs)

Pathogenic

VCV004526905

Review: criteria provided, single submitter

NM_024675.4(PALB2):c.1035_1038del (p.Lys346fs)

Pathogenic

VCV004526050

Review: criteria provided, single submitter

NM_024675.4(PALB2):c.1458del (p.Val487fs)

Pathogenic

VCV004294333

Review: criteria provided, single submitter

NM_024675.4(PALB2):c.355C>T (p.Gln119Ter)

Pathogenic

VCV004294293

Review: criteria provided, single submitter

NM_024675.4(PALB2):c.2368del (p.Gln790fs)

Pathogenic

VCV004294229

Review: criteria provided, single submitter


Recent Publications

There are 1,016 publications about PALB2 indexed in PubMed. Below are some recent papers:

ASO Author Reflections: Risk Management Strategies for Older Women With Germline Pathogenic Variants in BRCA1/2 and PALB2.

Melanson A, Wong SM

PMID: 41241707

2025 Nov 15

Ann Surg Oncol

Generation of functional noncanonical donor splice sites by +2T variants in breast cancer susceptibility genes: impact on clinical interpretation.

Llinares-Burguet I, Sanoguera-Miralles L, Bueno-Martínez E

PMID: 41230741

2025 Nov 13

J Pathol

Case Report: Metachronous pancreatic adenocarcinoma following HER2-positive breast cancer and the implications of non-BRCA germline variants with TP53-mutant disease.

Chen J, Zhou HC, Fan MH

PMID: 41229501

2025

Front Oncol

PARP Inhibitors in Metastatic Castration-resistant Prostate Cancer: Rationale, Mechanisms, and Clinical Applications.

Oudard S, Timsit MO, Maillet D

PMID: 41219112

2025 Nov 10

Eur Urol Oncol

Integrating Pathogenic Variants, Polygenic Risk Score, and Family History for Prostate Cancer Risk Estimation in Men of African Ancestry.

Chen F, Sheng X, Wang A

PMID: 41219045

2025 Nov 5

Eur Urol

View all 1,016 publications on PubMed →

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Trusted Data Sources

EnsemblMonarch InitiativeClinVarGeneReviewsPubMed

Last updated: 11/20/2025

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