Gene Information

DSC2

desmocollin 2 [Source:HGNC Symbol;Acc:HGNC:3036]

protein_codingChromosome 18ENSG00000134755

Overview

DSC2 variants are associated with 3 diseases including familial isolated arrhythmogenic ventricular dysplasia, left dominant form and familial isolated arrhythmogenic ventricular dysplasia, biventricular form and 1 others, with 14 documented clinical phenotypes.


Associated Diseases

The DSC2 gene is associated with 3 medical conditions, including:

familial isolated arrhythmogenic ventricular dysplasia, left dominant form

MONDO:0017401

familial isolated arrhythmogenic ventricular dysplasia, biventricular form

MONDO:0017402

familial isolated arrhythmogenic ventricular dysplasia, right dominant form

MONDO:0017403


Clinical Phenotypes

Research has identified 14 phenotypic features associated with DSC2 variants:

Sudden cardiac death

HP:0001645

Ventricular arrhythmia

HP:0004308

Palmoplantar keratoderma

HP:0000982

Right ventricular cardiomyopathy

HP:0011663

Autosomal recessive inheritance

HP:0000007

Palpitations

HP:0001962

Syncope

HP:0001279

Middle age onset

HP:0003596

Autosomal dominant inheritance

HP:0000006

Juvenile onset

HP:0003621

Late onset

HP:0003584

Woolly hair

HP:0002224

Dyspnea

HP:0002094

Young adult onset

HP:0011462


ClinVar Variants

ClinVar contains 10 variants associated with DSC2. Below are some notable variants:

NM_024422.6(DSC2):c.119C>T (p.Pro40Leu)

Uncertain significance

VCV004528258

Review: criteria provided, single submitter

NM_024422.6(DSC2):c.1889-3C>T

VCV004430945

NM_024422.6(DSC2):c.650C>T (p.Thr217Ile)

Uncertain significance

VCV004278732

Review: criteria provided, single submitter

NM_024422.6(DSC2):c.1397A>G (p.Asp466Gly)

Uncertain significance

VCV004088228

Review: criteria provided, single submitter

NM_024422.6(DSC2):c.550A>C (p.Asn184His)

Uncertain significance

VCV004087895

Review: criteria provided, single submitter


Recent Publications

There are 121 publications about DSC2 indexed in PubMed. Below are some recent papers:

The desmosomal cadherin Desmoglein-2 controls extracellular matrix expression and remodeling via NF-κB signaling in keratinocytes.

Hunter SE, Patel ZT, Mateo B

PMID: 41244075

2025

Front Cell Dev Biol

TGF-β signaling and tumor microenvironment dynamics in bladder cancer progression post-BCG therapy: a longitudinal single-nucleus RNA-seq study.

Lee SY, Lee YH, Kim TM

PMID: 41214597

2025 Nov 10

BMC Cancer

Epstein-Barr virus exploits desmocollin 2 as the principal epithelial cell entry receptor.

Wang H, Mou Z, Yeo YY

PMID: 41006833

2025 Nov

Nat Microbiol

Empagliflozin Preserves Cardiomyocyte Structural Homeostasis via the Stabilization of the Integrin α5-Desmocollin-2 Adhesion Axis in Sepsis-Induced Cardiomyopathy.

Qiao G, Lu Y, Wu J

PMID: 41002417

2025 Sep 16

Cells

Diagnostic and Prognostic Significance of Exercise Stress Testing in Desmosomal Arrhythmogenic Cardiomyopathy.

Castrichini M, Neves R, Garmany R

PMID: 40910968

2025 Aug 28

JACC Clin Electrophysiol

View all 121 publications on PubMed →

Analyze DSC2 Variants with AI

Get instant, comprehensive insights on DSC2 variants with Perception.

Get Started

Trusted Data Sources

EnsemblMonarch InitiativeClinVarGeneReviewsPubMed

Last updated: 11/20/2025

Perception Bio

Genomic intelligence.


© 2025 Perception Bio. All rights reserved.